ADAMTS13 and VWF activities guide individualized caplacizumab treatment in patients with aTTP

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Expression and significance of vWF, GMP-140 and ADAMTS13 in patients with aneurysmal subarachnoid hemorrhage.

OBJECTIVE The aim of this study was to investigate the role of the von Willebrand factor (vWF) in patients with aneurysmal subarachnoid hemorrhage (aSAH), platelet membrane glycoprotein-140 (GMP-140). The aim is also to discover the expression and clinical significance of von Willebrand factor (vWF) cleaving protease (ADAMTS13). PATIENTS AND METHODS 83 patients with aSAH were selected from Ja...

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Normal hemostasis is maintained by well-balanced performance of many factors in plasma, blood cells, and vascular wall cells. von Willebrand factor (VWF) is one of the plasma proteins that is involved in platelet adhesion and aggregation 1). VWF is synthesized in vascular endothelial cells and megakaryocytes, starting with a 350-kDa precursor. This polypeptide dimerizes in the endoplasmic retic...

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ژورنال

عنوان ژورنال: Blood Advances

سال: 2020

ISSN: 2473-9529,2473-9537

DOI: 10.1182/bloodadvances.2020001987